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OTC rabbit pAb
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ES14359
规格： 价格：
50µL ￥1280.00
100µL ￥1980.00
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Overview

产品名称: OTC rabbit pAb
反应性: Human; Mouse;Rat
别名: Ornithine carbamoyltransferase, mitochondrial (EC 2.1.3.3) (Ornithine transcarbamylase) (OTCase)
宿主: Rabbit
稀释比: WB 1:500-2000
免疫原: Synthesized peptide derived from human OTC AA range: 275-325
储存条件: -20°C/1 year
克隆性: Polyclonal
抗体亚型: IgG
浓度: 1 mg/ml
实测条带: 38kD
基因ID: 5009
蛋白序列: P00480
细胞定位: Mitochondrion matrix .
研究背景: This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also. [provided by RefSeq, Jul 2008],
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